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Morphofunctional features of the dental system in patients with Möbius and Williams syndromes
Abstract
The article examines the general somatic and phenotypic signs in patients with Williams and Möbius syndromes and also reveals the morphological and functional features of the dentofacial complex of patients with this pathology, which is based on congenital underdevelopment of the facial nerve nuclei and the hereditary chromosomal rearrangement. In the absence of radical treatment methods at present, physicians of various specialties need to improve their skills and knowledge about the developmental features of children with this pathology for the timely provision of not only medical, but also dental care to improve social adaptation and the quality of life of such patients.
About the Author
E. A. Chepik
Moscow State Medical and Dental University named after A.I. Evdokimov
Russian Federation
Russian Federation
Department of Orthodontics and Children's Prosthetics
Moscow
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Review
For citations:
Chepik E.A. Morphofunctional features of the dental system in patients with Möbius and Williams syndromes. Orthodontia. 2021;(2):31-37. (In Russ.)
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